1. Aortic dissection | 2. Annuloaortic ectasia | 3. Prophylactic | 4. Non-operated | |
---|---|---|---|---|
Patients | 10 | 9 | 9 | 17 |
Male | 4 | 6 | 6 | 3 |
Anthropometric (measured) | ||||
Height | 180.1 ± 10.1 | 183.9 ± 13.2 | 186.4 ± 13.7 | 180.2 ± 9.2 |
Lower segment (cm) | 95.8 ± 8.6 | 100 ± 11.8 | 99.1 ± 6.8 | 94.3 ± 5.9 |
Arm span (cm) | 190.3 ± 11.6 | 186 ± 17 | 192.6 ± 11.4 | 184.8 ± 7.5 |
Footsize | 42.9 ± 2.2 | 43 ± 3.3 | 44.2 ± 4.1 | 42.2 ± 2.5 |
Weight (kg) | 78.3 ± 13.4 | 71.9 ± 18.6 | 75.1 ± 19.3 | 69.6 ± 13.4 |
Anthropometric (calculated) | ||||
Upper segment (cm) | 84.3 ± 8.3 | 83.9 ± 9.2 | 87.3 ± 9.2 | 85.6 ± 6.8 |
Body Mass Index (BMI; kg/m2) | 24.2 ± 3.7 | 21 ± 4.2 | 21.5 ± 4.5 | 21.3 ± 3 |
Body surface area (m2) | 1.97 ± 0.2 | 1.91 ± 0.3 | 1.96 ± 0.3 | 1.86 ± 0.2 |
Upper segment - Lower segment ratio (USLS) | 0.89 ± 0.12 | 0.85 ± 0.14 | 0.88 ± 0.09 | 0.91 ± 0.09 |
Arm span - Height ratio (ASHR) | 1.06 ± 0.04 | 1.01 ± 0.04 | 1.04 ± 0.04 | 1.03 ± 0.03 |
Ghent nosology (%) | ||||
Mitral valve prolapse | 60 | 78 | 80 | 75 |
Pectus carinatum | 40 | 44 | 80 | 63 |
Pectus excavatum requiring surgery | 10 | 11 | 0 | 0 |
Reduced upper to lower segment ratio | 40 | 44 | 20 | 19 |
Increased arm span to height ratio | 70 | 11 | 10 | 19 |
Wrist sign | 90 | 67 | 80 | 81 |
Thumb sign | 80 | 67 | 100 | 94 |
Scoliosis of >20° or spondylolisthesis | 80 | 56 | 90 | 94 |
Severe scoliosis | 60 | 44 | 50 | 44 |
Reduced extension at the elbows | 20 | 0 | 0 | 13 |
Medial displacement of the medial malleolus causing pes planus | 30 | 22 | 70 | 69 |
Heel deformity | 0 | 11 | 10 | 13 |
Pectus excavatum of moderate severity | 20 | 22 | 40 | 31 |
Asymetric chest | 40 | 22 | 70 | 44 |
Joint hypermobility | 70 | 33 | 60 | 63 |
Highly arched palate with crowding of teeth | 60 | 33 | 70 | 56 |
Facial appearance | 50 | 22 | 60 | 38 |
Ectopia lentis | 30 | 11 | 30 | 31 |
Myopia over 3 diopters | 10 | 11 | 50 | 44 |
Spontaneous pneumothorax | 0 | 11 | 0 | 13 |
Striae atrophicae (stretch marks) | 100 | 44 | 70 | 56 |